A Series of Two Cases of Intraoral Malignancies in Patients with Xeroderma Pigmentosa
Ankit Dilip Mahuvakar, Darshan Premdas Meshram, Vijayalaxmi Kisanrao Ambulgekar, Mohsin Abdul Nabi Shaikh, Mohammad A Sameer
Citation Information :
Mahuvakar AD, Meshram DP, Ambulgekar VK, Shaikh MA, Sameer MA. A Series of Two Cases of Intraoral Malignancies in Patients with Xeroderma Pigmentosa. Int J Otorhinolaryngol Clin 2013; 5 (2):21-24.
Xeroderma pigmentosum (XP) is an autosomal recessive genetic disorder characterized by an increased frequency of skin cancer following minimal sunlight exposure.
Multiple basal cell carcinomas and other skin malignancies frequently occur at a young age in those with XP. In fact, metastatic malignant melanoma and squamous cell carcinoma are the two most common causes of death in XP victims.
This series represent rare presentations of malignancies in non-sun-exposed areas in such patients.
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