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VOLUME 9 , ISSUE 3 ( September-December, 2017 ) > List of Articles

CASE REPORT

Parry Romberg Syndrome: An Unusual Clinical Diagnosis

Gaurav Ashish, Mary John, Naina Picardo, Mary Kurien

Keywords : Blaschko\'s lines, En coup de sabre, Hemifacial atrophy, Parry Romberg syndrome

Citation Information : Ashish G, John M, Picardo N, Kurien M. Parry Romberg Syndrome: An Unusual Clinical Diagnosis. Int J Otorhinolaryngol Clin 2017; 9 (3):109-111.

DOI: 10.5005/jp-journals-10003-1278

License: CC BY-NC 4.0

Published Online: 01-12-2017

Copyright Statement:  Copyright © 2017; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Parry Romberg syndrome is a very rare clinical entity, manifested by chronic progressive hemifacial atrophy. The exact pathophysiology is poorly understood; however many hypotheses have been put forward to explain the above condition. It is a self-limiting condition and usually settles down after a few years of active facial resorption. This can clinically overlap with linear scleroderma also known as “en coup de sabre,” which is seen as a diagonal pit in the frontoparietal area. When the active phase is over, various treatment modalities have been employed such as fat, silicone or bone implants and pedicled flaps but with limited success. We present a case of Parry Romberg syndrome with involvement of sagittal sutures of the skull, an association that has been rarely reported. This case is being reported with aim of better understanding of this clinical entity regarding diagnosis and management.


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