An International Journal of Otorhinolaryngology Clinics

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VOLUME 16 , ISSUE 1 ( January-April, 2024 ) > List of Articles


Retrochrycoid Intermediate Extracardiac Rhabdomyoma: A Rare Cause of Dysphagia

Ana Nobrega Pinto, Eurico Monteiro, Eduardo Breda, Eduardo Ferreira

Keywords : Carbon dioxide lasers, Case report, Histology, Hypopharynx, Rhabdomyoma

Citation Information : Pinto AN, Monteiro E, Breda E, Ferreira E. Retrochrycoid Intermediate Extracardiac Rhabdomyoma: A Rare Cause of Dysphagia. Int J Otorhinolaryngol Clin 2024; 16 (1):25-28.

DOI: 10.5005/jp-journals-10003-1498

License: CC BY-NC 4.0

Published Online: 11-04-2024

Copyright Statement:  Copyright © 2024; The Author(s).


Introduction: Rhabdomyomas are rare benign tumors of the skeletal muscle. Regarding location, they can be subdivided into cardiac and extracardiac subtypes. Considering histological features, they can be classified as fetal, juvenile (intermediate), and adult. Case description: A 25-year-old male patient presented with a 3-month progressive dysphagia. Physical examination showed a smooth submucosal bulging of the right retrochrycoid region with anterior displacement of the ipsilateral larynx. Imaging studies [computed tomography (CT) scan and magnetic resonance imaging (MRI)] corroborated the findings in indirect laryngoscopy showing a well-defined nodular formation centered on the right retrochrycoid area that caused the anteromedial displacement of the right hemilarynx. The patient underwent transoral CO2 laser biopsy and the final histopathologic diagnosis was extracardiac juvenile rhabdomyoma. A transoral laser-assisted resection of the tumor was performed. Conclusion: Although muscle tumors of the hypopharynx are uncommon, rhabdomyoma should be considered in the differential diagnosis of submucosal masses in this region. Complete surgical excision is the treatment of choice.

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