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VOLUME 16 , ISSUE 1 ( January-April, 2024 ) > List of Articles

CASE REPORT

Congenital Mastoid Cholesteatoma with Posterior External Auditory Canal Erosion: A Case Report and Literature Review

Danny Kit Chung Wong, Aminuddin Saim

Keywords : Case report, Congenital cholesteatoma, Ear discharge, Mastoid, Rare

Citation Information : Wong DK, Saim A. Congenital Mastoid Cholesteatoma with Posterior External Auditory Canal Erosion: A Case Report and Literature Review. Int J Otorhinolaryngol Clin 2024; 16 (1):21-24.

DOI: 10.5005/jp-journals-10003-1495

License: CC BY-NC 4.0

Published Online: 11-04-2024

Copyright Statement:  Copyright © 2024; The Author(s).


Abstract

Background: Congenital cholesteatomas (CCs) are rare epidermal cysts that have been reported to occur most commonly in the middle ear and rarest in the mastoid cavity. They usually present in adulthood and are difficult to detect due to the lack of symptoms. Treatment is usually a canal wall up or down mastoidectomy with good success rates. Case description: We present a rare case of a mastoid CC with posterior external auditory canal wall erosion treated successfully with a simple canal wall-up mastoidectomy. Conclusion: Mastoid CCs still remain a rare entity with a relatively uncomplicated surgical approach. Clinical significance: Clinicians should high index of suspicion and a low threshold for a CT scan in patients with a history of an intermittently discharging ear, a narrowed ear canal, or a posterior canal wall fistula.

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