Congenital Mastoid Cholesteatoma with Posterior External Auditory Canal Erosion: A Case Report and Literature Review
Danny Kit Chung Wong, Aminuddin Saim
Keywords :
Case report, Congenital cholesteatoma, Ear discharge, Mastoid, Rare
Citation Information :
Wong DK, Saim A. Congenital Mastoid Cholesteatoma with Posterior External Auditory Canal Erosion: A Case Report and Literature Review. Int J Otorhinolaryngol Clin 2024; 16 (1):21-24.
Background: Congenital cholesteatomas (CCs) are rare epidermal cysts that have been reported to occur most commonly in the middle ear and rarest in the mastoid cavity. They usually present in adulthood and are difficult to detect due to the lack of symptoms. Treatment is usually a canal wall up or down mastoidectomy with good success rates.
Case description: We present a rare case of a mastoid CC with posterior external auditory canal wall erosion treated successfully with a simple canal wall-up mastoidectomy.
Conclusion: Mastoid CCs still remain a rare entity with a relatively uncomplicated surgical approach.
Clinical significance: Clinicians should high index of suspicion and a low threshold for a CT scan in patients with a history of an intermittently discharging ear, a narrowed ear canal, or a posterior canal wall fistula.
Warren FM, Bennett ML, Wiggins RH 3rd, et al. Congenital cholesteatoma of the mastoid temporal bone. Laryngoscope 2007;117(8):1389–1194. DOI: 10.1097/MLG.0b013e3180645d50.
Chauhan A, Wadhwa V, Rajan S, et al. Congenital choelasteatoma of the mastoid process: A case report. Otolaryngology Online Journal 2015;21(1):72–78. DOI: 10.4103/0971-7749.152875.
Giannuzzi AL, Merkus P, Talbah A, et al. Congenital mastoid cholesteatoma: Case series, definition, surgical key points, and literature review. Ann Otol Rhinol Laryngol 2011;120(11):700–706. DOI: 10.1177/000348941112001102.
Cvorovic L, Djeric D, Vlaski L, et al. Congenital cholesteatoma of mastoid origin–a multicenter case series. Vojnosanit Pregl 2014;71(7):619–622. DOI: 10.2298/VSP120130005C.
Derlacki EL, Clemis JD. Congenital cholesteatoma of the middle ear and mastoid. Trans Am Otol Soc 1965;53:208–231. PMID: 5834665.
El-Kholy AA, Cherry JR. Primary cholesteatoma of the mastoid presenting as cervical abscess. J Laryngol Otol 1989;103(1):92–93. DOI: 10.1017/s0022215100108114.
Luntz M, Telischi F, Bowen B, et al. Imaging case study of the month. Congenital cholesteatoma isolated to the mastoid. Ann Otol Rhinol Laryngol 1997;106(7 Pt 1):608–610. DOI: 10.1177/000348949710600715.
Cüreoglu A, Osma U, Oktay MF, et al. Congenital cholesteatoma of the mastoid region. J Laryngol Otol 2000;114(10):779–780. DOI: 10.1258/0022215001903906.
Lee JH, Hong SJ, Park CH, et al. Congenital cholesteatoma of mastoid origin. J Laryngol Otol 2007;121(11):e20. DOI: 10.1017/S0022215107000825.
Hidaka H, Ishida E, Kaku K, et al. Congenital cholesteatoma of mastoid region manifesting as acute mastoiditis: Case report and literature review. J Laryngol Otol 2010;124(7):810–815. DOI: 10.1017/S0022215109992209.
Janardhan N, Nara J, Peram I, et al. Congenital cholesteatoma of temporal bone with bezold's abscess: Case report. Indian J Otolaryngol Head Neck Surg 2012;64(1):97–99. DOI: 10.1007/s12070-011-0226-6.
Rajan KV, Santhi T. An unusual case of congenital cholesteatoma in the mastoid with epidural abscess and cutaneous fistula. Indian J Otolaryngol Head Neck Surg 2005;57(4):339–341. DOI: 10.1007/BF02907707.
Tabook SM, Abdel Tawab HM, Gopal NK. Congenital cholesteatoma localized to the mastoid cavity and presenting as a mastoid abscess. Case Rep Otolaryngol 2015;2015:305494. DOI: 10.1155/2015/305494.
Hong SM, Lee JH, Park CH, et al. Congenital cholesteatoma localized to the tip of the mastoid bone: A case report and possible etiology. Korean J Audiol 2014;18(2):85–88. DOI: 10.7874/kja.2014.18.2.85.
Rashad U, Hawthorne M, Kumar U, et al. Unusual cases of congenital cholesteatoma of the ear. J Laryngol Otol 1999;113(1):52–54. DOI: 10.1017/s0022215100143130.
Granato L, Silva CJ, Yoo HJ. Isolated congenital cholesteatoma of the mastoid process: A case report. Braz J Otorhinolaryngol 2012;78(4):133. DOI: 10.1590/S1808-86942012000400024.
Mevio E, Gorini E, Sbrocca M, et al. Congenital cholesteatoma of the mastoid region. Otolaryngol Head Neck Surg 2002;127(4):346–348. DOI: 10.1067/mhn.2002.128604.
Nagato T, Otaka R, Wada T, et al. Congenital cholesteatoma isolated to the mastoid presenting as stricture of the external auditory canal. Int J Pediatr Otorhinolaryngol 2012;76(5):754–756. DOI: 10.1016/j.ijporl.2012.02.032.
Thakkar KH, Djalilian HR, Mafee MF. Congenital cholesteatoma isolated to the mastoid. Otol Neurotol 2006;27(2):282–283. DOI: 10.1097/00129492-200602000-00023.
Davidoss N, Ha J, Banga R, et al. Delayed presentation of a congenital cholesteatoma in a 64-year-old man: Case report and review of the literature. J Neurol Surg Rep 2014;75(1):e113–e116. DOI: 10.1055/s-0034-1376200.