Facial Plexiform Neurofibroma as an Intraparotid Nodule: A Rare Case Presentation
Nishat Afroz, Divya Rabindranath, Shakeba Quadri, Rana K Sherwani
Neurofibromatosis, Parotid gland,Facial nerve
Citation Information :
Afroz N, Rabindranath D, Quadri S, Sherwani RK. Facial Plexiform Neurofibroma as an Intraparotid Nodule: A Rare Case Presentation. Int J Otorhinolaryngol Clin 2020; 12 (1):8-10.
CC BY-NC 4.0
Copyright © 2020; Jaypee Brothers Medical Publishers (P) Ltd.
Neurofibromas of salivary gland are very rare and account for only 0.4% of all salivary gland neoplasms. Plexiform type of neurofibromas are predominantly seen in a scenario of neurofibromatosis-1 (NF-1) association, but solitary plexiform neurofibroma has also been occasionally reported. We present a report of this variant in a 17-year-old male who is presented with a slow-growing painless swelling in the right preauricular region for 8-month duration. Microscopic examination revealed multiple cell types including Schwann cells, perineurial cells, axons, lymphocytes, mast cells, and endoneurial fibroblasts. Immunostaining with S100 confirmed the neural origin.
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