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VOLUME 11 , ISSUE 1 ( January-April, 2019 ) > List of Articles

CASE REPORT

Desmoid Fibromatosis of the Right Maxilla in an Infant: A Case Report

Vineet Kaul, Biswajyoti Hazarika, Manish Julaha, Nandini Hazarika, Shilpi Modi

Keywords : Pediatric tumors, Spindle cell neoplasm,Desmoid fibromatosis

Citation Information : Kaul V, Hazarika B, Julaha M, Hazarika N, Modi S. Desmoid Fibromatosis of the Right Maxilla in an Infant: A Case Report. Int J Otorhinolaryngol Clin 2019; 11 (1):19-21.

DOI: 10.5005/jp-journals-10003-1321

License: CC BY-NC 4.0

Published Online: 00-04-2019

Copyright Statement:  Copyright © 2019; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Desmoid fibromatoses are rare benign tumors that arise from the musculoaponeurotic tissues. They are locally aggressive and invade surrounding structures. We report a case of desmoid fibromatosis of the right maxilla in a 10-month-old male baby. This site of occurrence of desmoid tumor in an infant has not been reported previously in literature. Using Weber–Ferguson incision, wide excision with right upper alveolectomy was done to remove the tumor. Adjuvant chemotherapy consisting of a weekly regimen of vinblastine and methotrexate was given to achieve locoregional control and prevent disease recurrence.


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